| A case of bronchiectasis-related secondary renal amyloidosis with proteinuria |
|
Hyun Kyung Nam, Seo-Hee Rha, Soo Gul Lee, Seong Won Lee, Won Suk An, Seong Eun Kim, Ki Hyun Kim |
|
Department of Medicine, Sungkyunkwan University School of Medicine |
| 증례 : 단백뇨가 있는 기관지 확장증 환자에 발생한 이차성 신장 유전분증 1예 |
|
남현경&#;나서희&#;이수걸&#;이성원&#;안원석&#;김성은&#;김기현, Seo-Hee Rha, Soo Gul Lee, Seong Won Lee, Won Suk An, Seong Eun Kim, Ki Hyun Kim |
|
|
|
|
|
|
| Abstract |
|
Secondary amyloidosis is a disorder characterized by the deposition of amyloid A (AA) in multiple organs and tissues in the body. We report a case of bronchiectasis-related secondary renal amyloidosis with proteinuria. A 29-year-old male was admitted to our hospital for evaluation of foamy urine. He has been bothered from a large amount of mucopurulent sputum since 11 years. He had medical history of bronchiectasis and maxillary sinusitis. He had adenomatous goiter and showed hypothyroidism. Immunoelectrophoresis of serum and urine were nonspecific. Serum amyloid A level was high (243.0 ug/mL, reference value ; 0-8 ug/mL) and C-reactive protein was increased (3.8 mg/dL, reference value ; 0-0.5 mg/dL). Renal, thyroid and rectal biopsy revealed infiltration of homogenous material and showed apple-green birefringence in Congo-red stain. Apple-green birefringence in Congo-red stain of kidney, thyroid and rectum after potassium permanganate pretreatment was disappeared for the most part. We treated him with colchicine (1.2 mg per day).
After a year, his proteinuria was persisted, but renal function was normal.(Korean J Med 69:S900-S905, 2005) |
| Key Words:
Bronchiectasis, Amyloidosis, Proteinuria |
|
PDF Links
Full text via DOI
Download Citation
