Isolated Right Ventricular Noncompaction Accompanied by Right Ventricular Failure |
Sanghyok Lim1, Jihun Ahn2, Taehun O1, Donghyun Lee1, Minwoo Park1 |
1Department of Internal Medicine, Soonchunhyang University Cheonan Hospital, Soonchunhyang University College of Medicine, Cheonan, Korea 2Department of Internal Medicine, Soonchunhyang University Gumi Hospital, Soonchunhyang University College of Medicine, Cheonan, Korea |
우심실부전이 동반된 단독우심실비치밀화증 |
임상혁1, 안지훈2, 오태훈1, 이동현1, 박민우1 |
1순천향대학교 의과대학 순천향대학교 천안병원 내과 2순천향대학교 의과대학 순천향대학교 구미병원 내과 |
Correspondence:
Jihun Ahn, Tel: +82-54-468-9062, Fax: +82-54-468-3638, Email: jichoona@gmail.com |
Received: 23 January 2014 • Revised: 20 May 2014 • Accepted: 29 July 2014 |
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This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted noncommercial use, distribution, and reproduction in any medium, provided the original work is properly cited. |
Abstract |
Noncompaction of the ventricular myocardium is a rare congenital cardiomyopathy caused by arrest of normal endomyocardial embryogenesis. Isolated right ventricular noncompaction (IRNC) is an even rarer form of this disease. We report herein on a 68 year-old male diagnosed with IRNC who presented with right-sided heart failure, without involvement of the left ventricle. Diagnosis was achieved with the aid of echocardiography and ventriculography. Medical treatment including prescription of diuretics, a calcium channel blocker, and digitalis, improved both the symptoms and right ventricular function. |
Key Words:
Right ventricular noncompaction; Echocardiography; Right-sided heart failure |
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