Partial agenesis of dorsal pancreas with Castleman's disease in pancreatic tail area |
Sooyoung Park, Seungmin Bang, Myoung Hwan Kim, Han Jak Ryu, Jae Bock Chung, Woo Jung Lee, Si Young Song |
한림의대 한강성심병원 내과 |
증례 : 선천적 배측 췌장 부분 발육 부전증과 동반된 Castleman 병 1예 |
박수영, Seungmin Bang, Myoung Hwan Kim, Han Jak Ryu, Jae Bock Chung, Woo Jung Lee, Si Young Song |
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Abstract |
Agenesis of dorsal pancreas is a very rare congenital anomaly which comes from the failure of development of the body and tail of pancreas in embryogenesis. Castleman's disease is a rare lymphoid tumor which usually occurred in the mediastinum, but it is very uncommon in the retroperitoneal pancreatic tail area. We report a case of partial agenesis of dorsal pancreas with Castleman's disease in pancreatic tail area, mimicking a pancreatic tumor. A 46-year-old woman was admitted to our hospital with intermittent abdominal discomfort for 2 months. Computed tomography, magnetic resonance imaging, and endoscopic retrograde cholangiopancreatography (ERCP) revealed a tumor at distal pancreatic tail area, short pancreatic duct, and absence of pancreatic body and tail. The surgical excision of the tumor revealed hyaline-vascular type Castleman's disease.
Key Words : Castleman's disease, Agenesis, Pancreas |
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