A case of cardiac malignant fibrous histiocytoma treated by cardiac autotransplantation |
Hye Won Jang, Hyo Song Kim, Hyo Kyung Choi, A-Reum Han, Kay Hyun Park, , Geung Hwan Ahn, , Joon Oh Park |
경희대학교 의과대학 순환기내과학교실 |
증례 : 심장자가이식술로 치료한 좌심방의 원발성 악성섬유조직구종 1예 |
장혜원, 김효송, 최효경, 한아름, 박계현, 안긍환, 박준오, , Joon Oh Park |
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Abstract |
Primary cardiac tumors are rare findings and they are mostly benign. Malignant primary cardiac tumors make up 25% of the primary cardiac tumors and most of them are sarcomas. Malignant fibrous histiocytoma (MFH) is the most common soft tissue sarcoma in late adulthood, and it is an extremely rare sub-type of cardiac sarcoma. It is known that MFH displays a poor clinical course with complete resection being the most important prognostic factor for survival. We described here the case of a malignant fibrous histiocytoma of the heart in a 54-year-old woman who presented with dyspnea. The tumor was treated by mass excision via cardiac explantation and autotransplantation followed by adjuvant chemotherapy. This is the first report of cardiac autotransplantation in Korea.(Korean J Med 73:223-227, 2007)
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Key Words:
Malignant fibrous histiocytoma, Heart neoplasm, Autologous transplantation |
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