The Korean Journal of Internal Medicine

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Original Article
Korean J Med. 2007;72(1):90-94.
증례: 폐경 여성에서 반복적인 기흉으로 발현한 폐 림프관평활근종증 1예
박근민, , , , , ,
A case of lymphangioleiomyomatosis that presented with recurrent pneumothorax in a postmenopausal woman
Gun Min Park, Hyun Jee Kim, Jin Young Oh, Hyun Ju Lee, Sung Goo Han, Joo Hyun Kim, Young Soo Shim
고려대학교 의과대학 내과학교실


Abstract
Lymphangioleiomyomatosis is a rare disease which mostly occurs during the reproductive ages of premenopausal women. The presenting symptoms of lymphangioleiomyomatosis include cystic lung lesions, progressive dyspnea on exertion, and recurrent pneumothorax. HRCT shows bilateral diffusely scattered tiny cysts and PFT shows obstructive airflow limitation and decreased diffusion capacity. We report a case of lymphangioleiomyomatosis which presented with recurrent pneumothorax and characteristic cysts in HRCT. The diagnosis was confirmed by pathology. This is the first case of lymphangioleiomyomatosis diagnosed for a postmenopausal woman in Korea. Lymphangioleiomyomatosis must be considered in the diagnosis for a postmenopausal woman with characteristic symptoms and radiologic findings for Korean patients.(Korean J Med 72:90-94, 2007) Key Words : Lymphangioleiomyomatosis, Menopause, Pneumothorax

Keywords :Lymphangioleiomyomatosis, Menopause, Pneumothorax
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