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Original Article
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Korean J Med. 2009;76(2):234-237.
- 제1형 신경섬유종증 환자에서 발생한 흉강내 악성말초신경초종 1예
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최진이 &#; 김정훈 &#; 최자성 &#; 정재호 &#; 최정은 &#; 오화은 &#; 박찬, , , , , ,
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- An intrathoracic malignant peripheral nerve sheath tumor in a neurofibromatosis type 1 patient
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Jin Yi Choi, Jeong Hun Kim, Ja Sung Choi, Jae Ho Chung, Jeong Eun Choi, Hwa Eun Oh, Chan Sub Park
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- Abstract
- A malignant peripheral nerve sheath tumor (MPNST) is a rare soft tissue tumor defined as any malignant tumor arising
from or differentiating toward the cells of the peripheral nerve sheath. It is one of the malignant tumors associated with
neurofibromatosis type 1 (von Recklinghausen’s disease). They occur most commonly on the lower and upper extremities,
trunk, head, and neck, while intrathoracic tumors are very rare. We report an intrathoracic MPNST in a 66-year-old female
with neurofibromatosis type 1. (Korean J Med 76:234-237, 2009)
Keywords :Neurofibromatosis, Intrathoracic, Malignant peripheral nerve sheath tumor
