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Original Article
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Korean J Med. 2009;76(1):64-69.
- 좌심실을 침범한 부정맥유발성 우심실심근증 1예
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김영근, 김정희, 김동규, 정경태, 최유정, 이 상, 박순창
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- A case of arrhythmogenic right ventricular cardiomyopathy/dysplasia involving the left ventricle
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Young Keun Kim, Jeong-Hee Kim, Dong Gyu Kim, Kyoung Tae Jeong, Yu Jeong Choi, Sahng Lee, Soon Chang Park
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- Abstract
- Arrhythmogenic right ventricular cardiomyopathy (ARVC)/dysplasia is characterized by fibro-fatty replacement of the right
ventricular myocardium. A 19-year-old soldier was admitted with sudden cardiac arrest that presented as ventricular fibrillation requiring
cardiopulmonary resuscitation. His electrocardiogram (ECG) showed normal sinus rhythm with inverted T waves from
leads V1 to V4 and isolated premature ventricular beats with a left bundle branch block (LBBB) pattern. Echocardiography showed
that the right ventricle was enlarged with apical trabecular formation. The coronary angiogram was normal. Cardiovascular magnetic
resonance imaging (MRI) showed thinning and fatty substitution of both the right and left ventricular free walls. Ventricular
tachycardia (LBBB pattern) occurred frequently despite anti-arrhythmic drug treatment. His drug-resistant ventricular tachycardia
was treated with an implanted cardiac defibrillator.
Left ventricle involvement in ARVC is less common and more severe. Cardiac MRI is considered the best imaging technique for
evaluating the right ventricle and diagnosing ARVC. (Korean J Med 76:S64-S69, 2009)
Keywords :Arrhythmogenic right ventricular cardiomyopathy, Left ventricle
