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Original Article
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Korean J Med. 2009;76(1):228-233.
- 쇼그렌증후군 환자에서 발생한 무균성 농포증 1예
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임근준, 강봉구, 강석진, 김현숙, 김완욱
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- A case of amicrobial pustulosis of the folds in a patient with Sjögren’s disease
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Keun-Joon Lim, Bong-Koo Kang, Seok-Jin Kang, Hyun-Sook Kim, Wan-Uk Kim
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- Abstract
- Amicrobial pustulosis of the folds (APF) is a rare pustular eruption, which predominantly involves the cutaneous folds, including
the external auditory canals, scalp, and palms. It occurs in patients with a wide spectrum of autoimmune abnormalities. Systemic lupus
erythematosus is the autoimmune disorder observed most commonly in patients with APF. The etiology of APF is unclear, but
all reported cases have involved women of reproductive age when the eruptions first occurred.
This report describes a 34-year-old woman who presented with an acute pustular rash. Her medical history was unremarkable,
except for transitory dry eyes, dry mouth, and polyarthralgia for 1 year. Coalescing pustular lesions arising on erythematous skin,
forming crusted and eroded plaques, were observed, which predominantly affected the anterior chest, mainly the cutaneous folds.
The periorificial regions were also involved, including the nasal alae, mouth angles, and external auditory canals. Our patient had
the characteristic clinical and histopathological features of APF, in association with primary Sjögren’s syndrome (pSS). In conclusion,
we present a patient having APF associated with pSS. (Korean J Med 76:S228-S233, 2009)
Keywords :Amicrobial pustulosis of the folds, Sjö, gren’s disease
