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Original Article
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Korean J Med. 2009;77(1):240-244.
- 쇼그렌 증후군이 동반된 성인형 스틸병 1예
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정윤숙, 정상윤, 이광훈, 하유정, 백지현, 박용범, 이수곤
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- A case of adult-onset Still’s disease combined with Sjögren’s syndrome
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Yoon Suk Jung, Sang Youn Jung, Kwang Hoon Lee, You-Jung Ha, Ji-Hyeon Baek, Yong-Beom Park, Soo-Kon Lee
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- Abstract
- Sjögren’s syndrome is a chronic, slowly progressive autoimmune disease in which the exocrine glands are damaged by lymphocytic infiltration, resulting in xerostomia and xerophthalmia. Adult-onset Still’s disease (AOSD) is a multi-systemic inflammatory disorder, characterized by a high spiking fever, an evanescent salmon-colored rash, arthralgia or arthritis, lymphadenopathy, leukocytosis, and the involvement of various organs. We report the case of a 59-year-old female patient with Sjögren’s syndrome who presented with a fever of unknown origin. She was diagnosed with AOSD based on her high spiking fever, evanescent skin rash, arthralgia, lymphadenopathy, leukocytosis, sore throat, and hyperferritinemia after extensive investigations were performed to exclude other diseases. Her AOSD symptoms were successfully treated with high-dose glucocorticoid and methotrexate, without recurrence. We describe the case of a 59-year-old female patient with Sjögren’s syndrome and AOSD.
Keywords :Sjö, gren’s syndrome is a chronic, slowly progressive autoimmune disease in which the exocrine glands are damaged by lymphocytic infiltration, resulting in xerostomia and xerophthalmia. Adult-onset Still’s disease (AOSD) is a multi-systemic inflammator
