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Original Article
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Korean J Med. 2009;77(5):1258-1262.
- 특발성 후복막 섬유증 환자에 동반된 종격동 섬유증 1예
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최희정·김수민·최이령·송재욱·이유지·김윤구, , , , ,
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- A case of mediastinal fibrosis in a patient with idiopathic retroperitoneal fibrosis
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Hee Jung Choi, Soo Min Kim, E Ryoung Choi, Jae Uk Song, Yu Ji Lee, Yoon Goo Kim
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- Abstract
- Idiopathic retroperitoneal fibrosis is a rare disease characterized by proliferation of fibrous tissue with inflammation in the retroperitoneal
cavity, which is often associated with fibrosis of other organ systems. Multifocal fibrosclerosis is a term used to describe
a combination of multiple organ system fibrosis, such as mediastinal fibrosis, retroperitoneal fibrosis, orbital pseudotumor, sclerosing
cholangitis, and Reidel’s thyroiditis. Although there are several reports of retroperitoneal fibrosis associated with a combination
of fibrosis in variable organ systems, reports of combined retroperitoneal fibrosis and mediastinal fibrosis are rare. We report a case
of mediastinal fibrosis in a patient with idiopathic retroperitoneal fibrosis. (Korean J Med 77:S1258-S1262, 2009)
Keywords :Multifocal fibrosclerosis, Retroperitoneal fibrosis
